Diffuse esophageal spasm[DES] is a rare disease, and its surgical management is controversial. We experienced one case of diffuse esophageal spasm with a large epiphrenic diverticulum. We resected the diverticulum with right side approach and underwent extended esophageal myotomy from the apex of the chest to 3 cm above the diaphragm. And then we preserved the LES without antireflux procedure.