Chronic intestional pseudoobstruction syndrom is a rare clinical condition in which impaired intestinal peristalsis causes recurrent symptoms of bowel obstruction in the abvsence of a mechanical occlusion. This syndrome may involve variable segments of small or large bowel, and may be associated with urinary bladder retention. This study included 6 children(3 boys and 3 girls) of chronic intestinal obstruction. Four were symptomatic at birth and two were of the ages of one month and one year. All had abdominal distention and defication difficulty. Five had urinary bladder distention. Despite parenteral nutrition and surgical intervention(ileostomy or colostomy), bowel obstruction persisted and four patients expired from sepsis within one year. All had gaseous distention of small and large bowel on abdominal films. In small bowel series, consistent findings were variable degree of dilatation, decreased peristalsis (prolonged transit time) and microcolon or microrectum. This dis ase entity must be differentiated from congenital megacolon, ileal atresia and megacystis syndrome.