법랑질 형성부전증은 전치부 개교합과 같은 골격적인 문제를 자주 동반하며, 이러한 경우 구강악안면외과, 보철과, 보존과, 교정과 의사들이 함께 치료하여야 한다. 본 증례는 법랑질의 약화와 치아 우식증 등의 이유로 일반적인 교정치료를 시행할 수 없어 보철적 방법으로 치료하였다. 보존적, 보철적 방법을 이용하여 술전 교정과 같은 안정된 교합을 형성하였다. 악교정 수술을 시행하고 SAS 등을 이용하여 악간고정을 시행하여 양호한 결과를 얻을 수 있었다.
Amelogenesis imperfecta (AI) is a hereditary disease that affects enamel formation. The patients with AI have esthetic and functional problems due to damage of multiple teeth. So most AI patients resolve these problem through the conservative and prosthodontic treatments. In our case, It was difficult to obtain good results in means of conservative and prosthodontic treatments, because the AI patient had skeletal Class III malocclusion. Moreover, because of vertical dimension loss due to severe dental caries and maxillofacial skeletal disharmony, the ordinary prosthodontic treatment was troublesome. So we planned orthognathic surgery to resolve these problems. After the endodontic treatment, temporary restoration was delivered for stable post-operative occlusion. Then orthognathic surgery was done, and final restoration was delivered in stable period. We obtained satisfactory results in esthetic and functional aspects through multidisciplinary management(conservative treatment, prosthodontics and orthognathic surgery).
