- 복부에 발생한 악성 말초신경초종양
- ㆍ 저자명
- 소규섭,임영국,홍용택,김훈남,So. Kyu-Sub,Lim. Yeung-Kook,Hong. Yong-Taek,Kim. Hoon-Nam
- ㆍ 간행물명
- 大韓成形外科學會誌
- ㆍ 권/호정보
- 2011년|38권 6호|pp.886-889 (4 pages)
- ㆍ 발행정보
- 대한성형외과학회
- ㆍ 파일정보
- 정기간행물| PDF텍스트
- ㆍ 주제분야
- 기타
Purpose: Malignant peripheral nerve sheath tumor without neurofibromatosis type 1 is very rare neoplasm. Development in the superficial soft tissue is exremely rare. Authors experienced one rare case of primary malignant peripheral nerve sheath tumor developed on abdomen. The clinical and histologic findings were described. Methods: An 83-year-old man visited hospital with an $11{ imes}6.5{ imes}4.5$ cm sized ulcerated and hemorrhagic mass on abdomen. The tumor was localized in abdominal skin and started growing 3 years ago. Results: Wide excision with safety margin of 2 cm and limberg flap was done. The postoperative biopsy revealed a malignant peripheral nerve sheath tumor. There was no evidence of recurrence of tumor for 16 months. Conclusion: Malignant peripheral nerve sheath tumor is an aggressive malignant tumor. An abrupt enlargement of size, ulceration and bleeding are suggestive of malignant chnages of the tumor. We recommand early wide excision with enough safety margin as treatment of malignant peripheral nerve sheath tumor.